Amelogenesis imperfecta (Ai) (amelogenesis –
enamel formation; imperfecta – imperfecta) is a relatively
rare group of inherited disorders characterized by abnormal enamel
Dentinogenesis imperfecta (Di) represents a group
of hereditary conditions that are characterized by abnormal dentin
formation. These conditions can affect only the teeth or can be
associated with osteogenesis imperfecta.
The tricho-dento-osseous syndrome (TDO) (OMiM #190320)
is an autosomal sdominant condition that is named for the three
primarily affected tissues; hair, teeth and bone.